Transport of fatty acids into the mitochondrion CoA Acyl-CoA Carnitin Intermembran- Acyl-Carnitin 个 Carnitin Raum ●●● Matrix-Raum Carnitin Acyl.Carnitin← Carnitin Acyl-CoA CoA
Transport of fatty acids into the mitochondrion
0 R CH2 C=0 HO-CH S-CoA CH2 N Acyl-CoA CH3 CH3 Carnitin Carnitin-Acyl- transferase =0 0 CoA-SH 9 CH2 R-C-0-CH CH2 N: CH3 CH3 Acylcarnitin
β oxidation
b oxidation
Feeding dogs with o pheyl fatty acids Franz Knoop in Tubingen 1905 CH2 CH2 CH2 CH2 CH2 CH2 CH2 CH2 CH2 coo- C00- n=geradzahlig n =ungeradzahlig CH2 COO- COO- Phenylessigsaure Benzoesaure
Feeding dogs with o pheyl fatty acids Franz Knoop in Tübingen 1905
NH2 NH2 0 0 OH HO P-0-P-0-CH2 0 H2C-0 -0 0 0 NAD NADP structures H00 -P-0 Transfer of H2 (H+H) NAD*/NADP+
Oxidation of FADH2 by NAD NAD / NADP structures Transfer of H2 (H- + H+ )