Neurologic Muscular Disorders Zhou shuzhen(周水珍) Department of Neurology Childrens Hospital of FuDan University 复旦大学附属儿科医院
Neurologic & Muscular Disorders Zhou Shuizhen (周水珍) Department of Neurology Children’s Hospital of FuDan University
Part I: General Consideration o Anatomical and physiology features of the child cns o Neurological examination of children o Key facts about neurological disorders in children Infections of the cns Neurocutaneous syndromes Cerebral pals Progressive muscular dystrophy Seizure disorders(epilepsies non-epilepsy seizures) Convulsions Weakness (PBL) 回复旦大学上海医学院儿科学系
Part I: General Consideration Anatomical and physiology features of the child CNS Neurological examination of children Key facts about neurological disorders in children: – Infections of the CNS – Neurocutaneous syndromes – Cerebral palsy – Progressive muscular dystrophy – Seizure disorders (epilepsies & non-epilepsy seizures) – Convulsions & Weakness (PBL)
Physiologic and anatomical features of the child cns 1. Brain weight: at birth 6m ly 2y 4-6y adult 370700900100013001500(g) cerebra/pallium /cell number myelinization: fetal period w 4yrs 2. Spinal Cord weight: 2N6g(at birth) terminal 3(feta: L1(4y myelinization: 3y MADAM 回复旦大学上海医学院儿科学系
Physiologic and anatomical features of the child CNS 1. Brain - weight : at birth 6m 1y 2y 4-6y adult 370 700 900 1000 1300 1500 (g) - cerebra / pallium / cell number … - myelinization: fetal period ~ 4yrs. 2. Spinal Cord - weight: 2~6g (at birth) - terminal : L3 (fetal); L1(4y) - myelinization: 3y
Neurological examination of children A childs nervous system is continuous development Methods of neurological must be adapted to the childs developmental stage Neurological signs are altered by external factors o EXamination reveals presence of abnormalities\ . ay locations of lesions and clues of etiole 回复旦大学上海医学院儿科学系
Neurological examination of children A child’s nervous system is continuous development Methods of neurological must be adapted to the child’s developmental stage Neurological signs are altered by external factors Examination reveals presence of abnormalities, locations of lesions and clues of etiology
I General observation 1. General observation: Hyperactivity, attention, emotional state 2. Consciousness. Level; Quality 3. Speech language: Eye to eye contact Gestures Articulation; Understanding; Expression 4. Facies and Head: Size, shape of head Fontanelle, size tension Bruit transillumination of head 5. Neck: Movement, deformity, signs of meningeal irritation 6. Skin: Cafe au lait spots, telangiectasis, haemangiomas 回复旦大学上海医学院儿科学系
I. General observation 1. General observation: Hyperactivity, attention, emotional state 2. Consciousness: Level; Quality 3. Speech & language: Eye to eye contact ; Gestures Articulation; Understanding; Expression 4. Facies and Head: Size, shape of head; Fontanelle, size & tension; Bruit, transillumination of head 5. Neck: Movement, deformity, signs of meningeal irritation 6. Skin: Cafe au lait spots, telangiectasis, haemangiomas