举院 Clinical features 12 kEratoconjunctivitis Sicca ● Xerostomia o Involvement of other exocrine glands EXTraglandular manifestations 200 400 (00 BOD 1000 1400
Clinical features 11 ⚫Keratoconjunctivitis Sicca ⚫Xerostomia ⚫Involvement of other exocrine glands ⚫Extraglandular manifestations
f Extraglandular Manifestations ●Skin ● Polyarthralgia o Airways and lung disease ● Renal disease Gastrointestinal disease O Neurologic abnormalities 12
Extraglandular Manifestations 12 ⚫ Skin ⚫ Polyarthalgia ⚫ Airways and lung disease ⚫ Renal disease ⚫ Gastrointestinal disease ⚫ Neurologic abnormalities
举院 Skin 12 ● Dry skin ● Eyelid dermatitis ● Angular cheilitis Annular erythema ● Purpura o Urticarial vasculitis
Skin 13 ⚫ Dry skin ⚫ Eyelid dermatitis ⚫ Angular cheilitis ⚫ Annular erythema ⚫ Purpura ⚫ Urticarial vasculitis
Airways and lung disease ● Xerotrachea ● Bronchiolitis ●Ⅹ erobronchitis ● Lymphoma o Nonspecific interstitial pneumonitis( NSIP) o Lymphocytic interstitial peumonitis(LIP O Usual interstitial pneumonitis(UIP NSIP LIP UIP
Airways and lung disease ⚫ Xerotrachea ⚫ Xerobronchitis ⚫ Nonspecific interstitial pneumonitis (NSIP) ⚫ Lymphocytic interstitial peumonitis(LIP) ⚫ Usual interstitial pneumonitis (UIP) ⚫ Bronchiolitis ⚫ Lymphoma 14 NSIP LIP UIP
举院 12 Lymphocytic interstitial pneumonitis(LIP)in a 44-year-old woman with primary Sjogrens syndrome
15 Lymphocytic interstitial pneumonitis (LIP) in a 44-year-old woman with primary Sjögren’s syndrome